Doege–Potter-szindróma a mellhártya óriás malignus szoliter fibrosus tumorával

Autor: Zsolt Rozgonyi, Ibolya Soltész, József Kas, Gábor Grmela, Erika Lahm, Csaba Fehér, János Fillinger, Judit Varga, Attila Vágvölgyi, Zsuzsanna Papai, Pál Vadász, Attila Csekeő
Rok vydání: 2018
Předmět:
Zdroj: Orvosi Hetilap. 159:149-153
ISSN: 1788-6120
0030-6002
Popis: Abstract: Infrequent solitary fibrous tumours of the pleura are associated with hypoglycaemia only in a few percent of the cases; this condition is called Doege–Potter syndrome, named after its first descriptors. Our 63 years old male patient has previously undergone clinical treatment for intrathoracic fluid accumulation on the left side caused by a giant tumour-like mass in the lower left lobe detected by CT scan. In the course of further investigations performed due to increasing load-induced dyspnoea, lung core biopsy verified low grade sarcoma in the tumour. Tumour board suggested surgery. The patient was transferred from the intensive care unit into the operation theater due to increasing dyspnoea and repeated hypoglycaemic periods in rapidly worsening general condition. Pneumonectomy and removal of the tumour was performed on the left side. Histology showed solitary fibrous tumour of the pleura corresponding to Doege–Potter syndrome. The patient was discharged without complications and underwent adjuvant chemotherapy due to pleural dissemination of the tumour observed intraoperatively. One year after surgery the patient underwent surgical removal of a locally recurrent tumour. In spite of repeated chemotherapy local and multiplex contralateral pulmonary progression was observed. Three-year survival was noted from the time of the first surgery. Orv Hetil. 2018; 159(41): 149–153.
Databáze: OpenAIRE