Rapid Regression of Classic Clinical Signs of Cyanosis Accompanied by Disappearing Major Aortopulmonary Collaterals After Surgical Palliation Only in a 6-Year-Old Girl With Tetralogy of Fallot
| Autor: | Thomas Breymann, Harald Bertram, Dietmar Schranz, Thomas Jack, Armin Wessel, T. Mesud Yelbuz |
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| Rok vydání: | 2008 |
| Předmět: |
Cyanotic heart defect
congenital hereditary and neonatal diseases and abnormalities medicine.medical_specialty business.industry media_common.quotation_subject medicine.disease Shunt (medical) Surgery Stenosis medicine.anatomical_structure Tongue Physiology (medical) Internal medicine medicine Cardiology Ventricular outflow tract cardiovascular diseases Girl Cardiology and Cardiovascular Medicine business Oxygen saturation (medicine) Tetralogy of Fallot media_common |
| Zdroj: | Circulation. 118 |
| ISSN: | 1524-4539 0009-7322 |
| DOI: | 10.1161/circulationaha.108.788257 |
| Popis: | Tetralogy of Fallot is still the most common cyanotic heart defect and occurs in ≈1 in 3600 newborns or in 3.5% of the newborns with congenital heart disease.1,2 Since the first efforts of surgical repair in the 1950s, operation techniques with right ventricular outflow tract augmentation (RVOTA) and closure of ventricular septal defects have improved continuously. Today, in countries providing a high standard of medical care, patients with uncorrected tetralogy of Fallot presenting classic clinical signs of cyanosis are rare. A 6-year-old girl from Afghanistan with tetralogy of Fallot, a large malalignment ventricular septal defect, and high-grade infundibular pulmonary stenosis together with a hypoplastic pulmonary system had undergone a left-sided modified Blalock-Taussig shunt in her home country (exact date of surgery could not be determined). No further interventions were performed until the girl was transferred to Germany at 6 years of age. The clinical signs of chronic cyanosis at this time consisted of an extreme clubbing of the digits, especially of the toes, bluish skin, and a deep central cyanosis as indicated by blue lips and a cyanosed tongue (Figure 1A, 1D, and 1G). The oxygen saturation, measured transcutanously, was ≈65%. The hemoglobin level was 20 g/dL. Figure 1. Images … |
| Databáze: | OpenAIRE |
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