Hiperplasia nodular focal del hígado en niños y Trasplante Hepático
| Autor: | S Renato Sandoval, M Gloria Ríos, S Rubén Cárdenas, Z Mónica Zaror, A Montserrat Rius, T Domingo Videla, E Jorge Roque, K Juan Hepp, A Ricardo Espinoza, P Leopoldo Suárez, R Horacio Ríos, S Mario Cerda, L Rodrigo Valderrama |
|---|---|
| Rok vydání: | 2003 |
| Předmět: |
medicine.medical_specialty
Liver tumor medicine.diagnostic_test Orthotopic liver transplantation business.industry Encephalopathy Focal nodular hyperplasia medicine.disease Pediatrics Perinatology and Child Health Biopsy Ascites medicine Portal hypertension In patient Radiology medicine.symptom business |
| Zdroj: | Revista chilena de pediatría. 74 |
| ISSN: | 0370-4106 |
| Popis: | Focal nodular hyperplasia (FNH) is a benign tumour probably arising secondary to an altered vascularization of the hepatic parenchyma. It is rare in the paedriatric age group. We report a patient with FNH who underwent orthotopic liver transplantation (OLT) and we review the literature with respect to therapeutic approaches in treatment of FNH. A 15 year old boy presented with a palpable abdominal mass. Abdominal ultrasound and a CT scan showed multifocal tumours in both hepatic lobes. These were unresectable and a biopsy confirmed the diagnosis of FNH. The patient developed portal hypertension secondary to portal vein compression, with ascites, encephalopathy and renal failure. The decision between an expectant approach versus a surgical approach should be based on individual findings in each case. OLT is a therapeutic alternative in patients with benign unresectable liver tumours. |
| Databáze: | OpenAIRE |
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