Diffuse angiomatosis with hypersplenism

Autor: Andre de Vries, Meir Djaldetti, Jack Pinkhas, Doris Safra, Leah Dollberg
Rok vydání: 1968
Předmět:
Zdroj: The American Journal of Medicine. 45:795-801
ISSN: 0002-9343
DOI: 10.1016/0002-9343(68)90213-1
Popis: A patient with diffuse hemangiomatosis involving the spleen, liver, skin and conjunctivas, with pancytopenia due to hypersplenism, is described. Additional abnormalities were a mitral valve lesion, localized electroencephalographic disturbance and typical abortive coloboma of the retina. Splenectomy resulted in normalization of blood cell counts followed by polycythemia. The etiology of the combined congenital anomalies and of the postsplenectomy polycythemia is discussed.
Databáze: OpenAIRE