The Fontan Circulation: The Known, the Unknown and the Plausible

Autor: Marc Gewillig, Jacoba Louw
Rok vydání: 2013
Předmět:
Zdroj: Current Pediatrics Reports. 1:69-74
ISSN: 2167-4841
DOI: 10.1007/s40124-013-0017-5
Popis: The Fontan circulation is used as palliative surgery in the functionally univentricular heart. Due to the advances made in prenatal diagnosis, cardiac surgery, technology, and monitoring in complex congenital heart disease, survival rates have improved significantly. For this group of patients, the physiology and pathology remain challenging and eluding, even more so in the long-term follow-up. In the last decade pulmonary vascular resistance has been shown to be of utmost importance regarding cardiac output both at rest and during exercise. The aim of this article is to review the most recently published data, namely new concepts and our current understanding regarding the physiology; performance during exercise; the value of imaging modalities; and chronic liver pathology in the Fontan circulation.
Databáze: OpenAIRE