Juvenile Psammomatoid Ossifying Fibroma of the Orbital Roof: A Rare Cause of Proptosis among Children
| Autor: | Maysam Alimohamadi, Kasra Hendi, Saeed Dalfardi, Mohammad Rahmani, Amirhossein Larijani |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
medicine.medical_specialty
business.industry General Medicine Case presentation Histopathological examination Ossifying fibroma law.invention Frontal bone law Orbital roof Pediatrics Perinatology and Child Health Rare case Medicine Juvenile Surgery Neurology (clinical) Radiology business Ground glass |
| Zdroj: | Pediatric Neurosurgery. 55:163-168 |
| ISSN: | 1423-0305 1016-2291 |
| Popis: | Introduction: Juvenile psammomatoid ossifying fibroma (JPOF) is a rare bone tumor characterized by a predilection for the sinonasal region and a tendency to affect younger patients, with a potential for aggressive growth and high recurrence (30–56%). JPOF warrants complete surgical resection to avoid recurrence. Case Presentation: In this article, we report a young boy who presented with unilateral proptosis with an expansile bony tumor with ground glass appearance involving the left frontal bone and orbital roof on his images. Complete surgical resection was done, and histopathological examination revealed JPOF with abundant psammomatoid bodies. Discussion: This patient is a rare case of neurocranial JOPF and adds new features to the typical features already described for JPOF. |
| Databáze: | OpenAIRE |
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