Interruption of the aortic arch with patency of the arterial duct, discrete subaortic stenosis, restrictive ventricular septal defect and severe pulmonary hypertension—survival to adulthood and successful correction by balloon dilation and surgery
| Autor: | Satyavan Sharma, Robin J. Pinto, Nemish A. Shah |
|---|---|
| Rok vydání: | 1995 |
| Předmět: |
Aortic arch
medicine.medical_specialty business.industry Arterial duct General Medicine medicine.disease Pulmonary hypertension Balloon dilatation Restrictive ventricular septal defect Surgery medicine.artery Internal medicine Pediatrics Perinatology and Child Health cardiovascular system Balloon dilation Discrete Subaortic Stenosis medicine Cardiology Cardiology and Cardiovascular Medicine Subaortic stenosis business |
| Zdroj: | Cardiology in the Young. 5:367-369 |
| ISSN: | 1467-1107 1047-9511 |
| DOI: | 10.1017/s1047951100002870 |
| Popis: | We report a case of interruption of the aortic arch associated with patency of the arterial duct, restrictive ventricular septal defect, obstruction of the left ventricular outflow due to a discrete subaortic shelf and severe pulmonary arterial hypertension. The patient survived to adulthood, when a complete angiographic diagnosis was made. The subaortic obstruction was treated by percutaneous balloon dilation performed through a right brachial arteriotomy. Correction of the interrupted arch was carried out surgically using a woven Dacron graft from the aortic arch to the descending thoracic aorta associated with ligation of the duct. Hemodynamic studies after one year revealed a marked decrease in pulmonary vascular resistance and a sustained reduction in the gradient across the left ventricular outflow tract. The case is of interest in the light of the unusual survival and the success of staged management of this complex situation. |
| Databáze: | OpenAIRE |
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