Primary Hepatic Leiomyosarcoma A Space Occupying Lesion in the Liver: An Enigma for Diagnosis

Autor: Ashwini Kumar Setya, Irfan Ali Shera, Rajdeep B More, Sitendu Kumar Patel, Vivek Raj
Rok vydání: 2017
Předmět:
Zdroj: Journal of Gastroenterology, Pancreatology & Liver Disorders. 4:1-3
ISSN: 2374-815X
Popis: Primary hepatic leiomyosarcoma are rare soft tissue sarcomas with about only about 60 cases reported in the English literature [1]. Due to its rare existence and less studied, the diagnostic algorithms and standards of care have not been adequately defined. This has led to a delayed diagnosis and subsequently a poor prognosis and survival of such patients. We herein present a 72 year old lady with primary hepatic leiomyosarcoma treated with chemotherapy and attempt to delineate the line of management after reviewing the medical literature. Primary Hepatic Leiomyosarcoma is a rare primary hepatic malignancy which is usually a diagnosis of exclusion. The standard treatment guidelines are yet to be established; large cohort database is needed for better understanding of disease behaviour and management.
Databáze: OpenAIRE