Pulmonary Intravascular Lymphomatosis
| Autor: | J E Cox, Y G Hong, S Derdak, J G Walls, K M McCabe, K E O'Brien, J P Allerton |
|---|---|
| Rok vydání: | 1999 |
| Předmět: |
Pulmonary and Respiratory Medicine
medicine.medical_specialty Pathology Lung Vascular disease business.industry Respiratory disease Interstitial lung disease respiratory system Critical Care and Intensive Care Medicine medicine.disease Air trapping respiratory tract diseases Pulmonary function testing medicine.anatomical_structure Hounsfield scale medicine Radiology medicine.symptom Differential diagnosis Cardiology and Cardiovascular Medicine business |
| Zdroj: | Chest. 115:1207-1210 |
| ISSN: | 0012-3692 |
| Popis: | Intravascular lymphomatosis (IVL) is a rare lymphoid neoplasm that is typically of B-cell lineage and characterized by proliferation of malignant cells within small arterioles, capillaries, and venules. We report a patient with pulmonary IVL who presented clinically with progressive dyspnea, fever, and a dry cough. Pulmonary function tests revealed a marked decrease in diffusion capacity with airflow obstruction and severe air trapping. High-resolution CT (HRCT) of the chest with inspiratory and expiratory images revealed mosaic attenuation consistent with air trapping. Transbronchial biopsies revealed the diagnosis of IVL with capillary expansion in the alveolar and peribronchiolar interstitial tissue. IVL should be considered in the differential diagnosis of a patient with an interstitial lung disease, air trapping on pulmonary function tests, and mosaic attenuation on HRCT. Transbronchial biopsies may be the initial diagnostic procedure of choice. |
| Databáze: | OpenAIRE |
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