A CASE OF JUVENILE THORACIC AORTIC ANEURYSM ASSOCIATED WITH ATYPICAL COARCTATION
| Autor: | Sachito Fukuda, Yasuhiko Wanibuchi, Ikutaro Kigawa, Yoichi Yamashita, Toshihiro Ohata, Toshiaki Terada |
|---|---|
| Rok vydání: | 1999 |
| Předmět: |
Tunica media
Marfan syndrome medicine.medical_specialty Aorta business.industry Coarctation of the aorta medicine.disease Tunica intima Thoracic aortic aneurysm Surgery Aortic aneurysm medicine.anatomical_structure Aneurysm medicine.artery cardiovascular system Medicine cardiovascular diseases Radiology business |
| Zdroj: | Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association). 60:2329-2333 |
| ISSN: | 1882-5133 1345-2843 |
| Popis: | A 17-year-old woman underwent a general exploration because she came from a family of familial pheo-chromocytoma, when a chest CT scan revealed a throracic aortic aneurysm. The patient was admitted to the hospital for operation. A difference of about 30mmHg in systolic blood pressure between the upper and lower extremities was noted, and left subclavian vascular murmur was heard. Aortic fluoroscopy revealed a stricture of the aorta and a cystic mass 45mm in maximum diameter in the distal arch proximal to coarctation. At operation, the left subclavian artery and distal arch of the aorta were replacel with artificial vessels. Histopathologically, there were defects of of elastic fiber laver in the tunica intima and media in the aortic aneurysmic wall; and aortric wall which was seemingly normal involved necrotic change in the tunica media. These find-ings were similar to those of Marfan syndrome. There have been only 22 cases of aortic aneurysm associated with coarctation of the aorta including our case as far as we could review. Of these 22 cases, the aneurysm in the center of the coarctation is rarely noted and such cases acconut for about 18% (four cases). It is suggested that some congenital anomaly in the devel-opment might underlie in these cases. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|