Linfangioleiomiomatosis y esclerosis tuberosa: ¿una asociación casual o causal?

Autor:	R. Lana, R. Martínez-Cruz, J. M. F. Sánchez‐Alarcos, Myriam Calle, José Luis Álvarez-Sala
Rok vydání:	1998
Předmět:	Pulmonary and Respiratory Medicine medicine.medical_specialty business.industry Pulmonary disease High resolution Disease medicine.disease Dermatology Tuberous sclerosis Lung disease Childbearing age Lymphangioleiomyomatosis medicine business Open lung biopsy
Zdroj:	Archivos de Bronconeumología. 34:463-465
ISSN:	0300-2896
Popis:	Lymphangioleiomyomatosis (LAM) is a rare lung disease that mainly affects women of childbearing age. Pulmonary disease that is indistinguishable from LAM appears in 1% of patients with tuberous sclerosis (TS). At present we can not say whether we are looking at an association of two rare diseases or at a single disease with different clinical profiles. To date, open lung biopsy has been required for definitive diagnosis. We report the case of a women with TS and LAM in whom a diagnosis of pulmonary involvement was based on clinical signs and high resolution computerized tomography of the chest.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=doi_________::b1b573c836ec2f8024ad6dbcabad4f7a https://doi.org/10.1016/s0300-2896(15)30373-2 Zobrazit plný text záznamu Full Text from ScienceDirect