Dermatofibrosarcome protubérant de l’enfant

Autor: K. Ben Romdhane, Khaled Rahal, A. Ben Osman, M. Ben Abdallah, Moncef Mokni, Sondes Trojjet, I. Zaraa, D. El Euch, M. Ben Sassi, Maha Driss
Rok vydání: 2011
Předmět:
Zdroj: Archives de Pédiatrie. 18:23-27
ISSN: 0929-693X
DOI: 10.1016/j.arcped.2010.09.010
Popis: Dermatofibrosarcoma protuberans (DFSP) is a relatively rare skin neoplasm. Usually affecting adults, the incidence in children is even less frequent. Through a report of three pediatric cases of DFSP, we describe the particularities of this tumor in children. Three boys aged 8, 9, and 15 years presented with a firm nodular skin lesion of the trunk, varying in size from 1 to 5 cm. No previous trauma event had occurred. Diagnosis was confirmed in all cases by immunohistological study. Surgical excision was performed in all cases. No recurrence was evident during the follow-up period of, respectively, 15, 36, and 49 months. The DFSP is an infiltrative tumor of intermediate malignancy, with a limited potential for metastasis (
Databáze: OpenAIRE