| Autor: |
Katsuaki Maeda, Kunio Matsuoka, Toshiki Takahashi, Nobuhiro Fujita, Change Wong Kim, Akira Kitagawa, Kazuhiro Iwase, Yasuro Kishimoto |
| Rok vydání: |
1987 |
| Předmět: |
|
| Zdroj: |
The journal of the Japanese Practical Surgeon Society. 48:248-253 |
| ISSN: |
0386-9776 |
| DOI: |
10.3919/ringe1963.48.248 |
| Popis: |
Although many cases of traumatic intramural hematoma in the duodenum in children have been reported, nontraumatic intramural hematoma in the large intestine is extremely rare. Recently, we experienced a case of intramural hamatoma in the sigmoid colon associated with Marfan's syndrome of the incomplete type (forme fruste). This case is described with some comments based on the literature. The patient lacked ophthalmic symptoms and hereditary signs, but had skeletal anomalies. The complication of rupture of a dissecting aortic aneurysm due to median cystic necrosis accompanied by mucoid degeneration occurred after surgery. The patient's condition was thus considered to be Marfan's syndrome of the incomplete type. It is said that lesions in the cardiovascular system in Marfan's syndrome are attributable to abnormalities in the proteins composing the connective tissue or of the system for controlling protein production. The presence of a degenerative condition, Marfan's syndrome, may also have been involved in the formation of the intramural hematoma in the sigmoid colon of this patient. |
| Databáze: |
OpenAIRE |
| Externí odkaz: |
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