Bleeding Associated with Connective Tissue Disorders

Autor:	Dominder Kaur, Bryce A. Kerlin
Rok vydání:	2021
Předmět:	Marfan syndrome Pathology medicine.medical_specialty business.industry Connective tissue medicine.disease Loeys–Dietz syndrome medicine.anatomical_structure Coagulation Capillary fragility Ehlers–Danlos syndrome Osteogenesis imperfecta medicine Platelet business
Zdroj:	Management of Bleeding Patients ISBN: 9783030563370
Popis:	The interaction of platelets and coagulation proteins with subendothelial collagen at site of vessel injury is an essential part of the hemostatic pathway. For this reason, bleeding is common in some connective tissue disorders wherein the collagen protein structure is abnormal. This chapter reviews the bleeding manifestations in Ehlers-Danlos and related hypermobility disorders, Marfan syndrome, Loeys-Dietz syndrome, and osteogenesis imperfecta.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=doi_________::9d6be64f2cd0a0ab093f56d367351063 https://doi.org/10.1007/978-3-030-56338-7_20 Zobrazit plný text záznamu