Pentalogy of Cantrell with Sternum Agenesis—A Case Report
| Autor: | Marineia Vale, Elias Amorim, Antonio Vieira Dias Filho, Paulo Roberto Mocelin, Joseval Silva Lacerda, Petrucio Abrantes Sarmento, Rejane Albuquerque, Joel Fernando Sodré Bayma Silva, Victor Hugo Dorigo Castilho, Wildel Campos Ferreira, Camila Raposo, Nilo Antunes Sousa Filho |
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| Rok vydání: | 2020 |
| Předmět: |
medicine.medical_specialty
Tricuspid valve Sternum business.industry medicine.medical_treatment medicine.disease Costal cartilage Surgery Pentalogy of Cantrell Abdominal wall medicine.anatomical_structure Median sternotomy Agenesis cardiovascular system medicine Pericardium cardiovascular diseases business |
| Zdroj: | Open Journal of Thoracic Surgery. 10:1-5 |
| ISSN: | 2164-3067 2164-3059 |
| DOI: | 10.4236/ojts.2020.101001 |
| Popis: | Introduction: Pentalogy of Cantrell is a rare disorder described by Cantrell in 1958 and characterized by heart anomalies, involving defects of the diaphragm, abdominal wall, supraumbilical region and pericardium. Methods: We report a case of the disease that presented with agenesis of the sternum and partial absence of costal cartilage, treated by a multi-disciplinary team. Results: The patient underwent median sternotomy. An enlarged heart, compromising the pulmonary trunk and the right ventricle, and a left superior vena cava were identified. The right atrium was opened and an interventricular communication of around 10 mm in diameter was seen through the tricuspid valve. Following the repair of the heart defects, chondroplasty and placement of biological mesh (Bioway of Gore) were performed. Conclusion: A Successful surgical treatment for Cantrell Syndrome includes correction of the cardiac malformation, a good repair of thoracoabdominal wall. |
| Databáze: | OpenAIRE |
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