Ameloblastic fibrosarcoma of the mandible: case report and literature review
| Autor: | Julien Guiol, Franck Taugeron, Alain Hoornaert, Ségolène Le Cléac'h, Hélios Bertin, Benoit Piot, Emilie Hascoet, J. Longis, Corre Pierre |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
Ameloblastic Fibrosarcoma
medicine.medical_specialty medicine.medical_treatment 0206 medical engineering 02 engineering and technology Free flap 03 medical and health sciences Ameloblastic fibroma 0302 clinical medicine stomatognathic system medicine Dentistry (miscellaneous) Fibula Dental implant business.industry Dental prosthesis Mandible 030206 dentistry medicine.disease 020601 biomedical engineering Surgery stomatognathic diseases Periodontics Oral Surgery business Chemoradiotherapy |
| Zdroj: | Médecine Buccale Chirurgie Buccale. 23:164-168 |
| ISSN: | 2105-1011 1273-2761 |
| Popis: | Introduction: Ameloblastic fibrosarcoma is a rare malignant odontogenic tumor. Over 50% reported cases have histological evidence of ameloblastic fibroma at the same site. The mortality rate of the tumor is 19% and its recurrence rate is 37%, which mandates a total resection along with long-term follow-up. Observation: We present the case of a 14-year-old male diagnosed with ameloblastic fibrosarcoma, who underwent multiple stages of treatments and was followed up over 8 years. The initial management consisted of a total tumor resection with chemoradiotherapy. Then, for bone, soft, mucosal, and dental restoration after resection, mandibular reconstruction with a fibula free flap, onlay iliac graft, iliac graft fixation, facial lipofilling treatments (two), vestibular deepening procedures (two), and implant-supported dental prosthesis were performed. Comments and conclusion: This is the first case reported in the literature for the global management of mandibular ameloblastic fibrosarcoma, from oncological treatment to functional and aesthetic long-term rehabilitation. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|