Case Report of Prosthetic Treatment of a Young Patient Suffering Papilon-Lefever Syndrome
| Autor: | Mohammad Rastegar Khosravi, Masoumeh Rostamzadeh, Ghasem Omati Shabestari |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
medicine.medical_specialty
Alveolar bone destruction business.industry Hyperkeratosis 030206 dentistry Disease medicine.disease Surgery Prosthetic treatment stomatognathic diseases 03 medical and health sciences 0302 clinical medicine 030220 oncology & carcinogenesis Medicine business Permanent teeth |
| Zdroj: | International Journal of Clinical Medicine. :422-429 |
| ISSN: | 2158-2882 2158-284X |
| DOI: | 10.4236/ijcm.2017.86040 |
| Popis: | Papillon-Lefevre syndrome (PLS) is a rare recessive autosomal disease which occurs with palms and soles hyperkeratosis as well as primary and permanent teeth periodontal loss. Recently, it has been proved that a mutation at Cathepsin gene C is the genetic cause of PLS. All primary and permanent teeth of the patients are lost at ages 2 or 3 because of serious alveolar bone destruction. This paper presents a complete case of prosthetic treatment of an 8-year old girl with PLS. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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