Craniofacial Langerhans Cell Histiocytosis: A Rare Case Report

Autor:	Suriyakala M, Philips Mathew, Twinkle S Prasad, Sreela L S, Admaja K Nair
Rok vydání:	2021
Předmět:	Pathology medicine.medical_specialty Rib cage business.industry Mandible General Medicine medicine.disease Skull medicine.anatomical_structure Langerhans cell histiocytosis Rare case medicine Craniofacial Head and neck business Pelvis
Zdroj:	Journal of the College of Physicians and Surgeons Pakistan. 31:1239-1241
ISSN:	1681-7168 1022-386X
DOI:	10.29271/jcpsp.2021.10.1239
Popis:	Langerhans cell histiocytosis (LCH) is a rare haematological disorder characterised by accumulation and abnormal proliferation of bone marrow-derived Langerhans cells and mature eosinophils. The clinical presentation of patients with LCH may be localised or systemic, depending on the site and the degree of involvement. LCH may involve any bone, but the most commonly involved bones are long bones, pelvis, ribs, skull, vertebrae, and facial bones. In head and neck region, frontal and parietal bones are commonly involved followed by the jaws, with a predilection for mandible. In this report, we present a case of LCH involving the craniofacial bones in a 10-year boy, who presented initially with multiple ulcerative lesions on gingiva. Key Words: Craniofacial, Langerhans cell histiocytosis, Gingiva.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=doi_________::7fe64fbfa4852494f14d0f849360e8a9 https://doi.org/10.29271/jcpsp.2021.10.1239 Zobrazit plný text záznamu