The Peutz-Jeghers Syndrome and Malignant Tumor

Autor: Yoshio Mishima, Mahito Imajo, Katsuji Takemura, Nozomu Aoki, Hideyuki Ishida, Takeo Iwama
Rok vydání: 1990
Předmět:
Zdroj: Hereditary Colorectal Cancer ISBN: 9784431683391
DOI: 10.1007/978-4-431-68337-7_48
Popis: In our 19 cases of the Peutz-Jeghers (P-J) syndrome, we experienced two cases of carcinoma of the small intestine and two cases of uterine carcinoma. In 420 reported cases the of the P-J syndrome in Japanese literature there were 70 cases of gastrointestinal carcinoma ( mean age of 34.4 years) and 21 cases of extra gastrointestinal cancer (mean age of 41.2 years). Mucus producing adenocarcinoma was common patho-histological subdivision of gastrointestinal carcinoma (39%). Twelve of 20 cases of extra gastrointestinal cancer were uterine (9 cases) or ovarial (2 cases) carcinoma. Cervical adenocarcinoma (6 cases) was thought to be a specific cancer associated with the P-J syndrome.
Databáze: OpenAIRE