Uncommon association of Dandy-Walker type malformation and congenital chylous ascites – case report

Autor: Ioana Anca, Mirela Ritivoiu, Beata Acs, Florin Brezan
Rok vydání: 2008
Předmět:
Zdroj: Ultraschall in der Medizin - European Journal of Ultrasound. 29
ISSN: 1438-8782
0172-4614
DOI: 10.1055/s-2008-1079975
Popis: We present a 5 days old premature male infant with Dandy-Walker type malformation associated to congenital chylous ascites. Classically, posterior fossa cystic malformations have been divided into Dandy-Walker malformation, Dandy-Walker variant, mega cisterna magna, and posterior fossa arachnoid cyst. Dandy-Walker malformation, variant, and mega cisterna magna currently are believed to represent a continuum of developmental anomalies on a spectrum that has been termed the Dandy-Walker complex. Chylous ascites is uncommon in children. It is, however relatively more common in infancy. Congenital malformations of lymphatic system are responsible for 40% of cases. Idiopathic conditions accounts for 30% of cases and this condition said to have leaky limphatics. Secondary causes of chylous ascites include inflammatory, neoplastic, traumatic, non accidental injury, mechanical obstructions like malrotation, adhesive bands and incarcerated hernias.
Databáze: OpenAIRE