Kearns–Sayre syndrome associated with trifascicular block and QT prolongation
| Autor: | Panagiotis Korantzopoulos, Evaggelos Kountouris, Vasiliki Dimitroula, Eugenia Pappa, Konstantinos Siogas, Pavlos Karanikis, Dimitrios Patsouras |
|---|---|
| Rok vydání: | 2005 |
| Předmět: |
musculoskeletal diseases
medicine.medical_specialty Bundle branch block business.industry Heart block Long QT syndrome Trifascicular block Torsades de pointes medicine.disease QT interval Sudden cardiac death Kearns–Sayre syndrome Internal medicine Anesthesia medicine Cardiology Cardiology and Cardiovascular Medicine business |
| Zdroj: | International Journal of Cardiology. 101:147-150 |
| ISSN: | 0167-5273 |
| Popis: | Patients suffering from Kearns-Sayre syndrome (KSS) often develop conduction defects that may lead to syncope or sudden cardiac death. The association of conduction abnormalities with prolonged QT interval in these patients is very rare. We describe a patient with KSS and diabetes mellitus who suffered a torsades de pointes-induced syncopal attack, in the presence of trifascicular block and QT prolongation (QTc: 574 ms). The patient was successfully treated with permanent pacing. This case highlights that torsades de pointes represents a potential mechanism of syncope or sudden cardiac death in patients with KSS. |
| Databáze: | OpenAIRE |
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