Alternative Method for Full Oral Rehabilitation in Patients with Pycnodysostosis Syndrome: A Case Report
| Autor: | Pedro Rogério Camargos Pennisi, João Edson Carmo de Oliveira, Eduardo Buozi Moffa, Gustavo Vilela Oliveira, Andrea Cristina Zacarias Martins de Oliveira, Marcio Magno Costa, Luiz Renato Paranhos |
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| Rok vydání: | 2020 |
| Předmět: |
business.industry
0206 medical engineering Dentistry Hyperdontia 030206 dentistry 02 engineering and technology Enamel hypoplasia medicine.disease 020601 biomedical engineering Hypoplasia Chin Hypercementosis stomatognathic diseases 03 medical and health sciences 0302 clinical medicine medicine.anatomical_structure stomatognathic system Dysplasia Pycnodysostosis medicine Malocclusion business General Dentistry |
| Zdroj: | Clinical, Cosmetic and Investigational Dentistry. 12:131-139 |
| ISSN: | 1179-1357 |
| DOI: | 10.2147/ccide.s247614 |
| Popis: | Pycnodysostosis (PYCD) is a rare autosomal recessive skeletal dysplasia arising from a change in the production of the cathepsin K enzyme and it is also known as Maroteaux-Lamy Syndrome. The main changes in the buccal and maxillofacial region are modifications of the facial bones (leading to the loss of the mandibular angle due to micrognathia), deep palate, premature and/or delayed tooth eruption, hypopneumatization of the maxillary sinuses, chin hypoplasia, hypercementosis, enamel hypoplasia, hyperdontia, incomplete dentin calcification, root hypoplasia, pulp chamber obliteration, and increased free functional space. This paper aims to report a case of a patient with PYCD, in which are highlighted the oral manifestations of this syndrome and present an option of oral rehabilitative treatment through a removable overdenture made on natural tooth of the patient. The technique of dental coating through overdenture is a simple, viable and conservative alternative for oral rehabilitation of patients with large maxillomandibular discrepancies, as in cases of pycnodysostosis, especially in the presence of increased free space - characteristic of patients with this syndrome. The result was quite satisfactory both aesthetically and functionally and provided a better life quality for the patient. |
| Databáze: | OpenAIRE |
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