Pentalogy of Cantrell Associated With Thoracoabdominal Ectopia Cordis
| Autor: | Ze-wei Zhang, Qun-Jun Duan, Zhan Gao, Liang-long Ma, Li-yang Ying |
|---|---|
| Rok vydání: | 2009 |
| Předmět: |
Dextrocardia
congenital hereditary and neonatal diseases and abnormalities business.industry Anatomy medicine.disease Truncus arteriosus Pentalogy of Cantrell medicine.anatomical_structure Physiology (medical) Thoracoabdominal wall defect Thoracoabdominal ectopia cordis Ductus arteriosus cardiovascular system medicine Overriding aorta cardiovascular diseases Persistent left superior vena cava Cardiology and Cardiovascular Medicine business |
| Zdroj: | Circulation. 119 |
| ISSN: | 1524-4539 0009-7322 |
| DOI: | 10.1161/circulationaha.108.811000 |
| Popis: | A 4-day-old female infant with a partially extrathoracic heart in her supraumbilical abdominal wall (Figure 1A) presented with symptoms of tachypnea and mild cyanosis. Physical examination showed a thoracoabdominal wall defect with thoracoabdominal ectopia cordis. The xyphoid was absent and the sternum was short. Oxygen room air saturation was 85%. Chest x-ray showed dextrocardia and descensus of the heart contour to the right epigastrium (Figure 1B). Helical computed tomography (CT) demonstrated a ventral thoracoabdominal wall defect with the 2 ventricles protruding through the defective anterior diaphragm to epigastrium and positioned on the liver (Figure 1C through 1E). Truncus arteriosus and persistent left superior vena cava were observed on helical CT imaging (Figure 1C and 1F). Also present were ventricular septal defect, atrial septal defect, patent ductus arteriosus, and overriding aorta. Magnetic resonance imaging and echocardiography also successfully visualized truncus arteriosus (Figure 1G and 1H; also, see Figure 2 and online-only Data Supplement Movies I through III). Repeated echocardiogram confirmed these intracardiac findings and … |
| Databáze: | OpenAIRE |
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