IgG4-related disease

Autor: F. Martinez-Valle, M. Simó-Perdigó
Rok vydání: 2021
Předmět:
Zdroj: Revista Española de Medicina Nuclear e Imagen Molecular (English Edition). 40:107-114
ISSN: 2253-8089
Popis: IgG4-related disease (ER-IgG4) is a recognised systemic disease. It was described after patients diagnosed with autoimmune pancreatitis showed signs of extra-pancreatic disease. The clinical manifestation of these patients is subacute and is manifested by the appearance of pseudotumoral lesions, or inflammatory or fibrous tumours. Sometimes it can be serious as in the case of patients with cholangitis or large vessel vasculitis. Diagnostic criteria include, among others, serum IgG4 elevation and/or histological parameters. The 18F-FDG-PET/CT is useful in the initial diagnosis, biopsy guidance as well as in the assessment of response to therapy. It usually responds to steroid therapy.
Databáze: OpenAIRE