Tabique vaginal transverso diagnosticado en dos hermanas. Reporte de dos casos

Autor: María J Boillos Calvo, Gonzalo González García, Patricia Bretón Hernández, Anna Miralles Puigbert
Rok vydání: 2017
Předmět:
Zdroj: Archivos Argentinos de Pediatria. 115
ISSN: 0325-0075
Popis: Transverse vaginal septum is a disorder that would arise from a failure in the fusion and/or channeling of the urogenital sinus and the mullerian ducts with low frequency but with a significant impact on the health of patients. The treatment is surgical and it will depend on the location and thickness of the septum. Sometimes, it described a female sex-limited autosomal recessive transmission but few cases of family association have been reported. We present the cases of two sisters who had this rare entity 5 years apart and were diagnosed by the presentation of an intense hypogastric abdominal pain at the age of 11 and 12 years when they had a Tanner stage III pubertal development and primary amenorrhea.
Databáze: OpenAIRE