OHVIRA syndrome in an infant girl
| Autor: | Mazen O. Kurdi, Ahmed Al-Sayyad, Jameela A. Kari, Sherif M. El-Desoky, Ruba Sahab |
|---|---|
| Rok vydání: | 2019 |
| Předmět: |
Gynecology
medicine.medical_specialty Kidney Exploratory laparotomy business.industry Urinary system medicine.medical_treatment General Engineering Hydrometrocolpos Renal function urologic and male genital diseases medicine.disease medicine.anatomical_structure medicine Menarche business Renal agenesis Hydronephrosis |
| Zdroj: | Asian Journal of Pediatric Nephrology. 2:88 |
| ISSN: | 2589-9309 |
| Popis: | Obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) is a rare congenital urogenital anomaly, which usually presents after menarche. We report a 3-month-old infant who presented with recurrent urinary tract infections (UTI) and had an abdominal lump. Radiological investigations revealed absent right kidney, hydronephrotic left kidney, and a cystic pelvic mass. Exploratory laparotomy revealed hydrometrocolpos which was evacuated. During 1-year follow-up, hydronephrosis decreased, there were no further UTI, and kidney function remained normal. Our case illustrates that OHVIRA syndrome may present in early infancy with UTI, renal anomalies, and pelvic mass. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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