| Autor: |
Homoud Al-Sabah, F.R.C.P.C. Marie-France Demierre M.D., Salem Al-Shemmari, Hejab Al-Ajmi, Qasem A. Alsaleh, Arti Nanda, Muhammad Elkashlan |
| Rok vydání: |
2010 |
| Předmět: |
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| Zdroj: |
Pediatric Dermatology. 27:607-613 |
| ISSN: |
0736-8046 |
| DOI: |
10.1111/j.1525-1470.2010.01129.x |
| Popis: |
Mycosis fungoides (MF) is rare in children and adolescents. This study was aimed to determine the clinicoepidemiologic features of juvenile onset (≤18 yrs) MF in Kuwait. Thirty-six children and adolescents (≤18 yrs) with MF registered in a referral photobiology unit for cutaneous lymphomas between July 1991 and June 2009 were included in this study. Children and adolescents were observed to constitute 16.6% of the total number of patients with MF, with 97% of patients of Arab ethnicity. The age-adjusted incidence rate of MF in children and adolescents among the total population was 0.29/100,000 persons/year. Among 36 Arab children and adolescents, boys outnumbered girls by 1.25:1. Mean and median age at onset of disease was 9 years, and age at diagnosis was 13 years. Patch stage disease was the most common clinical variant (75%) with 56% with pure hypopigmented MF-variant. The majority of patients (75%) had stage IB (TNM and B staging) disease. The study highlights a high prevalence and incidence of juvenile MF in Kuwait with a predominantly hypopigmented presentation. |
| Databáze: |
OpenAIRE |
| Externí odkaz: |
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