A difficult airway approach in a merosin-deficient congenital muscular dystrophy patient: a case report
| Autor: | Ana Pinto Carneiro, Jorge Pelicano Paulos, Catarina Cruz, Vanessa Artilheiro |
|---|---|
| Rok vydání: | 2021 |
| Předmět: |
Pediatrics
medicine.medical_specialty business.industry medicine.medical_treatment General Medicine Perioperative medicine.disease 03 medical and health sciences 0302 clinical medicine Intravenous anesthesia 030202 anesthesiology medicine Restrictive lung disease Airway management Muscular dystrophy business Airway Difficult airway Merosin deficient congenital muscular dystrophy |
| Zdroj: | Brazilian Journal of Anesthesiology (English Edition). |
| ISSN: | 0104-0014 |
| DOI: | 10.1016/j.bjane.2021.03.018 |
| Popis: | Merosin-deficient muscular dystrophy is caused by an autosomal recessive mutation on laminin-α2 gene characterized by severe progressive muscle weakness associated with neuromuscular scoliosis and restrictive lung disease. In this case report, we describe an alternative airway approach performed in a child with anticipated difficult airway and merosin-deficient muscular dystrophy. Significant anesthetic implications may increase the perioperative risk, requiring accurate knowledge to anticipate an adequate management and provide patient-safety strategies. |
| Databáze: | OpenAIRE |
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