Ivemark syndrome with obstructed supracardiac TAPVC- case report

Autor:	Chaitanya Challa, Vala Ramgopal Rao, Sravani Vemuri, C Sudharshan Raj
Rok vydání:	2021
Předmět:	medicine.medical_specialty business.industry Ivemark syndrome Medicine business Surgery
Zdroj:	International Journal of Contemporary Pediatrics. 8:389
ISSN:	2349-3291 2349-3283
DOI:	10.18203/2349-3291.ijcp20210137
Popis:	Heterotaxy disorder is a disturbance in the usual left and right distribution of the thoracic and abdominal organs. Ivemark syndrome is one such heterotaxy disorder. It is a rare disorder which affects males more than females with majority of cases presenting in the neonatal period mainly due to complex congenital cardiac disease. Here is a case report of rare disorder of the neonate with Ivemark syndrome with obstructed supracardiac total anomalous pulmonary venous connection (TAPVC). Management of obstructed supracardiac TAPVC is complicated as PGE1 infusion is contraindicated and immediate surgical correction is advised.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=doi_________::6147f77db9cd596718628ae3a71ef884 https://doi.org/10.18203/2349-3291.ijcp20210137 Zobrazit plný text záznamu