Chirurgie secondaire des craniosténoses et faciocraniosténoses

Autor: Michel Zerah, S. Haber, Brigitte Fauroux, Eric Arnaud, Syril James, Matthieu P. Robert, H. Khonsari, C. Legros, Giovanna Paternoster, Arnaud Picard, V. Viot-Blanc, Vincent Couloigner, M.-P. Morisseau-Durand, P H Meyer, Valérie Cormier-Daire
Rok vydání: 2019
Předmět:
Zdroj: Annales de Chirurgie Plastique Esthétique. 64:494-505
ISSN: 0294-1260
DOI: 10.1016/j.anplas.2019.07.001
Popis: Secondary surgeries for single craniosynostosis surgeries are mainly esthetic refinements rather than functional indications. However, cranioplasties for bone defects correction or insufficient corrections may be undertaken. Management of syndromic craniosynostoses usually requires multiple surgical interventions, the sequence of which might vary per the genetic mutation. It is commonplace to start with posterior vault expansion before age 6 months, then treat cerebellar tonsillar herniation by the age of twelve months, and delay fronto-facial monobloc advancement until at least 18-24 months of age. Ventricular shunting is preferably avoided or delayed. Failure to respect these guidelines can significantly complicate the subsequent management. Primary fronto-orbital advancement or early facial osteotomy type Le Fort3, may compromise the subsequent fronto-facial monobloc advancement. However, this salvage secondary monobloc may be undertaken in some instances despite previous anterior osteotomies with a higher morbidity.
Databáze: OpenAIRE