Hereditary Hemorrhagic Telangiectasia or Osler-Weber -Rendu Syndrome: Management of Epistaxis in 4 Cases
| Autor: | Salina H, Gendeh Bs, Lim Ps |
|---|---|
| Rok vydání: | 2020 |
| Předmět: |
education.field_of_study
Gastrointestinal tract medicine.medical_specialty business.industry Population General Medicine Dermatology medicine.anatomical_structure medicine Nail (anatomy) Osler-Weber-Rendu Syndrome medicine.symptom Presentation (obstetrics) education Telangiectasia business Nose Rare disease |
| Zdroj: | IIUM Medical Journal Malaysia. 17 |
| ISSN: | 2735-2285 1823-4631 |
| Popis: | Hereditary Hemorrhagic Telangiectasia, also known as Osler-Weber-Rendu Syndrome is an autosomal dominant disorder causing systemic abnormalities of the vascular structure. There are multiple arteriovenous malformations present in the skin and mucosal surface of the nail beds, nose, gastrointestinal tract, lungs and brain. Epistaxis is the common presentation symptom, which may require multiple hospital admissions and blood transfusions. It is extremely rare disease in our population. We report 4 cases of HHT who presented to us with moderate to severe epistaxis and how we managed these patients. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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