The PEComa Tumor: Could It Be Considered an Independent Neoplasmic Entity?
| Autor: | Maria Del Carmen Velasco Fernández, Carmen González-Tejero, Gonzalo Quesada Segura, Rut Bernardo Vega, Fernando Vázquez Camino, José Manuel Mayor González |
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| Rok vydání: | 2005 |
| Předmět: |
medicine.medical_specialty
Pathology Angiomyolipoma Hysterectomy business.industry medicine.medical_treatment Uterus Obstetrics and Gynecology medicine.disease Perivascular Epithelioid Cell Surgery medicine.anatomical_structure Lymphangioleiomyomatosis Eosinophilic medicine Neoplasm business Epithelioid cell |
| Zdroj: | Journal of Gynecologic Surgery. 21:161-166 |
| ISSN: | 1557-7724 1042-4067 |
| Popis: | The tumors known as "PEComas" or perivascular epithelioid cell tumors are a group of lesions composed exclusively or predominantly of epithelioid cells. These cells have abundant clear to eosinophilic granular cytoplasm and are HMB-45 positive. Other members of this family are some of the forms of angiomyolipoma and lymphangioleiomyomatosis, as well as clear-cell "sugar" tumor. We describe a case of these features localized in the uterus of a 34- year-old female. She was operated on with the suspicion of uterine myoma; the histological examination revealed perivascular epithelioid cell tumor (PEComa). A total hysterectomy and bilateral salpingo-oophorectomy was performed. Because of the extremely small number of cases, PEComas are considered of uncertain malignant potential. We also discuss the possibility of considering PEComa as an independent entity or whether it has to be classified as an unusual variety of epithelioid smooth-muscle neoplasm. (J GYNECOL SURG 21:161) |
| Databáze: | OpenAIRE |
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