Pulmonary Alveolar Proteinosis in a Hypogammaglobulinemic Infant
| Autor: | J. Ben-Ari, J. Sandbank, Y. Rivlin, Y. Yaniv, R. Efrat, T. Schonfeld, Ben-Zion Garty |
|---|---|
| Rok vydání: | 1998 |
| Předmět: |
Pulmonary and Respiratory Medicine
business.industry Congenital cytomegalovirus infection Hydroxychloroquine Cellular immunodeficiency respiratory system medicine.disease Hypogammaglobulinemia Intravenous Immunoglobulins Pediatrics Perinatology and Child Health Immunology medicine Immunology and Allergy business Pulmonary alveolar proteinosis Pneumonitis medicine.drug Rare disease |
| Zdroj: | Pediatric Asthma, Allergy & Immunology. 12:151-156 |
| ISSN: | 1557-7767 0883-1874 |
| Popis: | Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by deposition of a surfactant-like material in the alveolar spaces. It is often fatal in infants. PAP has been reported in association with cellular immunodeficiency syndromes, but not with hypogammaglobulinemia. We present a 10-month-old child with hypogammaglobulinemia in whom PAP developed following cytomegalovirus pneumonitis. Treated with massive one-lung lavage, intravenous immunoglobulins, and hydroxychloroquine, she had prolonged remissions. |
| Databáze: | OpenAIRE |
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