Fibroma of the interventricular septum with bilateral obstruction of the ventricular outflow/tracts

Rok vydání: 2021
Předmět:
Zdroj: Medical Visualization. 25:140-146
ISSN: 2408-9516
1607-0763
DOI: 10.24835/1607-0763-855
Popis: Heart fibroma accounts for about 5% of all primary neoplasms and is registered in children in 80% of cases. The ventricles or interventricular septum (IVS) are most often affected; in half of cases, the tumor has intracavitary growth. The clinical picture of the disease and its prognosis depend on the size and location of the tumor. The most unfavorable is the defeat of the IVS, since it causes obstruction of the output tract of one of the ventricles. Being localized in IVS, can involve a conducting system of heart, thereby increasing risk of sudden death.A retrospective study of a case of cardiac fibroma in a child aged 4.5 months, confirmed by echocardiography, magnetic resonance imaging and successfully operated on in the Central Federal District Center of Penza, is presented. A large tumor, localized in the IVS, caused atypical obstruction of the outflow tracts of both ventricles simultaneously. In the domestic and foreign literature, hemodynamic disturbances of only one of the ventricles are described, and we did not find a single case with simultaneous obstruction of both tracts. The possibility of MRI in the diagnosis of heart tumors has been shown.
Databáze: OpenAIRE