Popis: |
Desmoid fibromatosis (DF) is a rare intermediate soft tissue tumour characterised by myofibroblastic cell proliferation. Although desmoid tumours are locally very infiltrative, they hold no metastatic potential, and a significant proportion of cases naturally regress if simply observed. Considering this, a first-line policy of active observation should be adopted in all cases (with appropriate analgesia as required). If disease progression or symptoms require intervention, several other non-surgical treatments, including radiotherapy and chemotherapy, should be considered prior to surgery. This makes close collaboration with a soft tissue tumour MDT essential when managing these complex patients. |