Présentation inhabituelle d’une granulomatose de Wegener
Autor: | Fatma Boussema, Ouahida Cherif, S. Ketari Jamoussi, E. Turki, L. Rokbani, Samir Kochbati, B. Ben Dhaou, M. Maamar |
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Rok vydání: | 2010 |
Předmět: |
Kidney
medicine.medical_specialty medicine.diagnostic_test business.industry medicine.medical_treatment Gastroenterology Renal function medicine.disease Scintigraphy Nephrectomy Surgery Nephritic syndrome Venous thrombosis medicine.anatomical_structure Internal Medicine medicine Right Renal Artery Radiology Vasculitis business |
Zdroj: | La Revue de Médecine Interne. 31:e16-e18 |
ISSN: | 0248-8663 |
Popis: | We report an unusual case of Wegener's granulomatosis revealed by spleen infarction and complicated by reno-vascular hypertension. A 33-year-old man with a history of spleen infraction and cerebral venous thrombosis was admitted for malignant hypertension, renal failure and nephritic syndrome. On Doppler renal ultrasonography, ostial stenosis of the right renal artery was evidenced. Right kidney was non functional on scintigraphy and the patient underwent a right nephrectomy. Granulomatous vasculitis of the right renal artery was found but anti-neutrophilic cytoplasmic antibodies were absent. The diagnosis of Wegener's granulomatosis was suspected. The patient was treated with cyclophosphamide, corticosteroids and plasma exchanges, and renal function markedly improved. |
Databáze: | OpenAIRE |
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