Primary Retroperitoneal Müllerian Adenocarcinoma: Report of Two Cases Treated With Radical Surgery

Autor: Kerim Kaban, Dogan Vatansever, Emine Handan Zeren, Yasemin Bolukbasi, S Misirlioglu, Cihangir Celik, Cagatay Taskiran, T. Arslan
Rok vydání: 2021
Předmět:
Zdroj: Journal of Obstetrics and Gynaecology Canada. 43:242-246
ISSN: 1701-2163
Popis: Background Primary retroperitoneal Mullerian adenocarcinoma (PRMA) is a very rare type of primary retroperitoneal tumour. Case 1 A 45-year-old woman presented with left lower extremity swelling and pain. Imaging revealed that the tumour had invaded the left common iliac vein and artery, internal and external iliac arteries, sciatic and obturator nerves, and pelvic wall. Case 2 A 37-year-old was admitted with pelvic pain. Imaging showed the tumor at the left iliac bifurcation infiltrating the internal iliac artery and left sciatic, obturator, and femoral nerves. Both of these patients were treated with radical surgery that achieved no visible tumour at the end of the operation. Conclusion There is no guideline for the diagnosis and management of this entity due to its rarity. These cases should be managed at highly specialized centres with expertise in radical surgery.
Databáze: OpenAIRE