David’s procedure in a patient with haemophilia
Autor: | Debashish Sahu, Aju Jacob, Vijit Koshy Cherian, Bashi V. Velayudhan, Krithika Ramaprabhu |
---|---|
Rok vydání: | 2017 |
Předmět: |
Pulmonary and Respiratory Medicine
medicine.medical_specialty Haemophilia A 030204 cardiovascular system & hematology Haemophilia law.invention 03 medical and health sciences 0302 clinical medicine law hemic and lymphatic diseases medicine.artery Ascending aorta medicine Cardiopulmonary bypass business.industry Vascular surgery medicine.disease Surgery Cardiac surgery 030228 respiratory system Coagulation Cardiothoracic surgery Anesthesia Cardiology and Cardiovascular Medicine business |
Zdroj: | Indian Journal of Thoracic and Cardiovascular Surgery. 33:247-248 |
ISSN: | 0973-7723 0970-9134 |
DOI: | 10.1007/s12055-017-0499-9 |
Popis: | Haemophilia A is a sex-linked recessive disorder characterized by deficiency of factor VIII. Cardiac surgery in haemophiliac patients is challenging in terms of bleeding, due to the requirement of heparin, cardiopulmonary bypass and hypothermia. The complex coagulation disturbances triggered by cardiopulmonary bypass are further exacerbated by the lack of adequate haemostasis in haemophiliacs. We present this case report of a young haemophiliac with a dilated ascending aorta and aortic root, who underwent a David’s operation successfully. We establish that with meticulous haemostasis, adequate factor VIII replacement protocol and perioperative management of factor VIII levels, good results can be achieved in these patients. |
Databáze: | OpenAIRE |
Externí odkaz: |