Peutz-Jeghers Syndrome- A Rare Cause of Duodenal Obstruction: A Case Study in a Tertiary Care Hospital in Bangladesh

Autor:	Dr. Susankar Kumar Mondal, Dr. Noor Mahammad, Dr. Umme Habiba Dilshad Munmun, Dr. Koushik Sikdar, Dr. Tarafder Mohammad Atiquzzaman
Rok vydání:	2022
Předmět:	General Medicine
Zdroj:	Scholars Journal of Medical Case Reports. 10:697-699
ISSN:	2347-6559 2347-9507
DOI:	10.36347/sjmcr.2022.v10i07.024
Popis:	Peutz-Jeghers syndrome (PJS) is a rare hamartomatous polyposis of the gastrointestinal GI) tract, sometimes associated with pigmentation around lips and oral mucosa. The case of a 4-year-old girl who presented with duodenal obstruction is reported. Along with multiple small polyps in the duodenum, a large polyp was found to be the cause of the duodenal obstruction. Histologically most of the polyps were hamartoma. PJS is a rare autosomal dominant disease. Most patients have recurrent episodes of polyposis in the gastrointestinal tract causing gastrointestinal obstruction as well as these patients have an increased risk of both gastrointestinal and non-gastrointestinal malignancy and need regular screening.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=doi_________::20177842e2d872a9c9d59eddc8626bb8 https://doi.org/10.36347/sjmcr.2022.v10i07.024 Zobrazit plný text záznamu