A case of Wilms tumor with right ventricular extension of tumor thrombus
| Autor: | Ayşe Gülnur Tokuç, Rabia Ergelen, Kıvılcım Karadeniz Cerit, Mustafa Çakan, Koray Ak |
|---|---|
| Rok vydání: | 2017 |
| Předmět: |
Thorax
Chemotherapy medicine.medical_specialty business.industry Mechanical Engineering medicine.medical_treatment Metals and Alloys Wilms' tumor Abdominal distension medicine.disease Inferior vena cava Surgery medicine.anatomical_structure medicine.vein Mechanics of Materials Ventricle cardiovascular system Medicine cardiovascular diseases Radiology Stage (cooking) medicine.symptom business Vein |
| Zdroj: | Case Reports in Internal Medicine. 4:60 |
| ISSN: | 2332-7251 2332-7243 |
| Popis: | Primary renal tumors comprise 6% of all childhood cancers. Wilms tumor is the most common primary renal tumor in pediatric age group and the peak age of diagnosis is 3-4 years. In 10% of cases tumor extension into hepatic vein and inferior vena cava can be seen. But tumor extension into whole inferior vena cava, right atrium and right ventricle is only seen in less than 1% of patients. A 2-year-old girl was admitted to the hospital because of abdominal distension that was noticed by the parents two weeks ago. Imaging studies revealed that she had a mass at the right renal lodge which was favoring to Wilms tumor and on thorax tomography tumor thrombus was seen in the whole inferior vena cava, right atrium and right ventricle. Neoadjuvant chemotherapy was given for 7 weeks. On the 8th week of diagnosis, under cardiopulmonary bypass, surgical operation by pediatric and cardiovascular surgery teams for primary renal tumor and for cavo-atrial tumor thrombus was performed. Pathological examination of the mass was reported as stage 3 diffuse anaplastic Wilms tumor. The patient completed 24 weeks of chemotherapy protocol and she is being followed for 15 months without any morbidity. We present our case to emphasize the importance of multidisciplinary approach in Wilms tumor with cardiac extension. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
|