Severe pulmonary vein stenosis in association with IgG4 gammopathy: An unusual case

Autor:	Thomas Theologou, Jonathan Fergusson, Mohamed Moneer ElSaegh, Amer Harky, Ursula Earl
Rok vydání:	2020
Předmět:	Pulmonary and Respiratory Medicine medicine.medical_specialty Weakness business.industry fungi Disease 030204 cardiovascular system & hematology medicine.disease 03 medical and health sciences 0302 clinical medicine 030228 respiratory system Gammopathy parasitic diseases Palpitations Breathing Medicine Surgery IgG4-related disease Histopathology Radiology medicine.symptom Cardiology and Cardiovascular Medicine Pulmonary vein stenosis business
Zdroj:	Journal of Cardiac Surgery. 35:689-691
ISSN:	1540-8191 0886-0440
Popis:	IgG4-related disease (IgG4-RD)is a multifactorial and systemic immune-mediated disease. Pulmonary vein stenosis related to IgG4 is a rare entity. We report a case of a 57-year-old male who presented with vague symptoms of weakness, easy fatigue, shortness of breathing, chest tightness, and occasional palpitations. The patient was admitted, and investigations were arranged in the form of anterior mediastinotomy and pleural biopsies were taken to look for a possible diagnosis. The histopathology was reported as IgG4-related immunopathy. A transoesophageal echocardiogram was performed and this showed severe stenosis of left superior pulmonary vein. In patients with rare pathologies such as IgG4-RD, a transesophageal can be a useful diagnostic aid especially in patients with severely impaired renal functions which does not allow utilization of contrast computed tomography.
Databáze:	OpenAIRE
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