Von Hippel-Lindau disease (VHL-syndrome)
| Autor: | D G Bel'tsevich, M Iu Iukina, A N Tiul'pakov, E A Troshina |
|---|---|
| Rok vydání: | 2012 |
| Předmět: |
Pathology
medicine.medical_specialty endocrine system diseases business.industry Endocrinology Diabetes and Metabolism Central nervous system Cancer Disease urologic and male genital diseases medicine.disease female genital diseases and pregnancy complications Broad ligament Pheochromocytoma medicine.anatomical_structure Hemangioblastoma Medicine cardiovascular diseases Von Hippel–Lindau disease Pancreatic cysts business neoplasms |
| Zdroj: | Problems of Endocrinology. 58:34-41 |
| ISSN: | 2308-1430 0375-9660 |
| DOI: | 10.14341/probl201258234-41 |
| Popis: | Von Hippel-Lindau disease is a hereditary tumour syndrome associated with the earlier development of a variety of benign and malignant neoplasms, such as hemangioblastomas of the central nervous system and retina, tumours of the internal ear, renal carcinoma and cysts, pheochromocytoma, neuroendocrine tumours, pancreatic cysts, epididymal and broad ligament cystadenomas in men and women respectively. Von Hippel-Lindau disease is considered to be the most common cause of hereditary renal cancer. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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