Anesthetic management of craniosynostosis repair in a 13-month-old boy with Apert syndrome

Autor:	Hardika Mangal, Prashant Santlani
Rok vydání:	2021
Předmět:	musculoskeletal diseases Fibrous joint medicine.medical_specialty business.industry Branchial arch Apert syndrome medicine.disease Craniosynostosis Surgery Skull medicine.anatomical_structure Maxilla medicine Syndactyly business Congenital disorder
Zdroj:	Indian Journal of Case Reports. 7:214-216
ISSN:	2454-1303 2454-129X
DOI:	10.32677/ijcr.2021.v07.i05.013
Popis:	Apert syndrome is a congenital disorder characterized by malformations of the skull, face, hands, and feet. It is a form of acrocephalosyndactyly. It is classified as a branchial arch syndrome, affecting the first branchial (or pharyngeal) arch, the precursor of the maxilla and mandible. Presently described is a case of 13-month-old boy diagnosed with apert syndrome. French pediatrician Eugene Apert described Apert syndrome in 1906. The purpose of this report is anesthetic management of craniosynostosis repair in this child under general anesthesia. Craniosynostosis, the premature fusion of skull sutures, results in failure of normal bone growth perpendicular to the suture and the compensatory growth at other suture sites, which results in an abnormally shaped head. Anesthetic challenges include management of a difficult airway, airway hyperreactivity, possibility of raised intracranial pressure, blood loss, blood transfusion, and its associated complications.
Databáze:	OpenAIRE
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