Idiopathic Fibrosing Mediastinitis Causing Pulmonary Hypertension with Improvement by Steroid Treatment

Autor: Choon-Sik Park, Sang Do Lee, Sung Jun Eo, Yong Hoon Kim, Eun Seo Park, Gi Hyun Seo, Bo Yong Jung, Joo Ock Na, Jae Sung Cho, Soo Taek Uh, Young Tong Kim, Mi Hye Oh
Rok vydání: 2006
Předmět:
Zdroj: Tuberculosis and Respiratory Diseases. 61:74
ISSN: 1738-3536
DOI: 10.4046/trd.2006.61.1.74
Popis: 3 Idiopathic fibrosing mediastinitis is, an uncommon cause of pulmonary hypertension this is characterized by excessive fibrosis of the mediastinum with an unknown etiology. Steroid t herapy has been suggested for individuals with progressive symptoms, bu there is littlet data demonstrating the efficacy of such therapy are lacking. We present a case of pulmonary hypertension secondary to a compression of a main pulmonary artery by fibrosing mediastinitis which was confirmed by a biopsy with a thoracotomy. The chest CT scan and 2D echocardiography performed before and after a trial of steroid therapy demonstrated improvement after steroid therapy. (Tuberc Respir Dis 2006; 61: 74-79)
Databáze: OpenAIRE