Xantogranuloma juvenil solitario congénito. Caso clínico
Autor: | Andrea Bettina Cervini, Paola C Stefano, Marcela Bocian, Adrián M. Pierini, G. Leticia Lazarte, Verónica Solernou |
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Rok vydání: | 2017 |
Předmět: |
medicine.medical_specialty
Pathology business.industry Juvenile xanthogranuloma medicine.disease Abdominal wall Lesion Histiocytosis medicine.anatomical_structure Touton giant cell Pediatrics Perinatology and Child Health Medicine Abdomen Histopathology Differential diagnosis medicine.symptom business |
Zdroj: | Archivos Argentinos de Pediatria. 115 |
ISSN: | 0325-0075 |
DOI: | 10.5546/aap.2017.e9 |
Popis: | Juvenile xanthogranuloma is a bening pathology and it represents the most common form of non-Langerhans cell histiocytosis. It is characterized by the presence of papules or firm nodules of a pinkish or yellow-brownish nature, which mainly compromise the skin and, exceptionally, other organs. It is a self-limited entity having a spontaneous regression during the first five years of life. We report the case of a one-month-old patient who presented a congenital tumor in the abdomen, whose histopathology showed the presence of multinucleated giant Touton cells, which are typical of this pathology. We emphasize the rare occurrence of this type of lesion and the importance of the multiple differential diagnosis to be taken into account due to the age of the patient and the characteristics of the lesion. |
Databáze: | OpenAIRE |
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