Maladie d'Erdheim-Chester Forme multiviscérale révélée par une exophtalmie
| Autor: | Y. Pinaudeau, I. Rozenberg, G. Coscas, J. Hazard, D. Larde, F. Koenig, B. Brun, Y. Raulo, J. Wechsler |
|---|---|
| Rok vydání: | 1986 |
| Předmět: |
Chemotherapy
medicine.medical_specialty Exophthalmos business.industry medicine.medical_treatment Gastroenterology Autopsy medicine.disease Dermatology Vinblastine Osteosclerosis medicine.anatomical_structure Internal Medicine Medicine Retroperitoneal space Differential diagnosis medicine.symptom business Retroperitoneal xanthogranuloma medicine.drug |
| Zdroj: | La Revue de Médecine Interne. 7:311-317 |
| ISSN: | 0248-8663 |
| DOI: | 10.1016/s0248-8663(86)80016-9 |
| Popis: | Erdheim-Chester disease is a rare visceral xantho-granulomatosis, the 17th case of which is reported here. The initial symptom, bilateral exophthalmos, was uncommon. The picture was completed by a retroperitoneal xanthogranuloma and by bilateral and symmetrical osteosclerosis of the long bones. The lack of X-bodies at electron microscopy differentiated the disease from Hand-Schuller-Christian disease. The patient's condition improved with chemotherapy (vinblastine and doxorubicin) combined with corticosteroid therapy. After a 5-month remission period, he died of an intercurrent infection. No autopsy was performed. |
| Databáze: | OpenAIRE |
| Externí odkaz: |
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