PEUTZ JEGHERS SYNDROME PRESENTING WITH ACUTE INTESTINAL OBSTRUCTION: A RARE CASE REPORT WITH REVIEW OF LITERATURES

Autor: P. K. Hota, G. Narasimha Reddy, G. Rajasekhar, C. Nalini Mohan
Jazyk: angličtina
Rok vydání: 2015
Předmět:
Zdroj: Bali Medical Journal, Vol 4, Iss 2, Pp 98-101 (2015)
ISSN: 2302-2914
2089-1180
Popis: Background: Peutz-Jeghers syndrome is a rare genetic disorder presenting in young age with mucocutaneous pigmentation and hamartomatous polyposis. Method: We report a case of Peutz-Jeghers syndrome in a 16 year old boy presenting with acute intestinal obstruction. Results: Imaging studies revealed intussusception. He had mucocutaneous pigmentation and multiple hamartomatous polyps which were diagnosed histologically. The unusual presentation of the case and its successful management has prompted us to report the case with literature review.
Databáze: OpenAIRE