| Popis: |
Marfan syndrome is an autosomal dominant connective tissue disorder characterized by skeletal, cardiovascular, and ocular anomalies The iridocorneal endothelial syndrome typically manifests in early to middle adulthood, usually occurs in women, and is almost always unilateral. The purpose of this article is to report a rare case of both syndromes. An ocular association not previously described in a left eye in a 35 years old patient. The visual acute was 0,4 Dp. iris atrophy, pupilar ectopic, endothelial iris and secundary glaucoma with ocular hypertension. In a fundoscopic study we found optic atrophy. Conclussion: Is rare the association to the Marfan Syndrome with the Iridocorneal endothelial syndrome. |
