PHACES Syndrome with Intestinal Hemangiomatosis

Autor:	Vrkić Boban, Ivona, Lozić, Bernarda, Stričević, Luka, Čulo Čagalj, Ivana, Skelin Glavaš, Ana, Krželj, Vjekoslav
Jazyk:	angličtina
Rok vydání:	2019
Předmět:	body regions PHACES syndrome neonate intestinal hemangiomatosis
Zdroj:	Acta Dermatovenerologica Croatica Volume 27 Issue 4
ISSN:	1847-6538 1330-027X
Popis:	We present a rare case of a neonate with PHACES syndrome (posterior fossa malformations, large facial hemangiomas, cerebral arterial anomalies, cardiovascular anomalies, eye anomalies and sternal clefting or supraumbilical raphe) and diffuse hemangiomatosis of the ileum, presenting with multiple intestinal perforations and peritonitis. The infant was successfully treated with propranolol and methylprednisolone as well as octreotide, tranexamic acid, and supportive therapy for massive intestinal bleeding.
Databáze:	OpenAIRE
Externí odkaz:	https://explore.openaire.eu/search/publication?articleId=dedup_wf_001::e62b01a14963fa7036e346d95657bc12 https://hrcak.srce.hr/file/419938 Zobrazit plný text záznamu