Enfermedad neuromuscular: evaluación clínica y seguimiento desde el punto de vista neumológico
| Autor: | Martínez Carrasco C, Villa Asensi JR, Luna Paredes MC, Osona Rodríguez de Torres FB, Peña Zarza JA, Larramona Carrera H, Costa-Colomer J |
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| Rok vydání: | 2014 |
| Předmět: |
Duchenne muscular dystrophy
Ventilación no invasiva Neumología pediátrica Neuromuscular disease Spinal muscular atrophy Enfermedad neuromuscular Distrofia muscular de Duchenne Atrofia muscular espinal Trastorno respiratorio del sueño Non-invasive ventilation Chronic respiratory failure Sleep-disordered breathing Pediatric respiratory medicine Insuficiencia respiratoria crónica |
| Zdroj: | ANALES DE PEDIATRIA r-FSJD. Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu instname r-FSJD: Repositorio Institucional de Producción Científica de la Fundació Sant Joan de Déu Fundació Sant Joan de Déu |
| ISSN: | 1695-4033 |
| Popis: | Patients with neuromuscular disease are an important group at risk of frequently suffering acute or chronic respiratory failure, which is their main cause of death. They require follow-up by a pediatric respiratory medicine specialist from birth or diagnosis in order to confirm the diagnosis and treat any respiratory complications within a multidisciplinary context. The ventilatory support and the cough assistance have improved the quality of life and long-term survival for many of these patients. In this paper, the authors review the pathophysiology, respiratory function evaluation, sleep disorders, and the most frequent respiratory complications in neuromuscular diseases. The various treatments used, from a respiratory medicine point of view, will be analyzed in a next paper. |
| Databáze: | OpenAIRE |
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